The concept of Behcet's syndrome is progressing as a systemic disease involving multiple organs and system. In 1937 Behcet described a chronic relapsing triple symptom complex of recurrent oral ulceration, genital ulceration, and ocular
inflammation.
Other manifestation of the syndrome include arthritis, cutaneous vasculitis, thrombophlebitis, epididymitis, ulcers of the gastrointestinal tract, and meningoencephalitis.
Recently, we experienced a case of intestinal Behcet's syndrome with obstructive ileus. A 21-year-old female patient with incomplete type of Behcet's syndrome suffered from abdominal pain, aphthous stomatitis, and genital ulceration.
The frequent obstructive site of intestine is ileocecal area.
The mucosa of ileum shows large geographic ulcer with fibrous wall thickening and multiple small round ulcers with punched-out in appearance.
After ileocecotomy and administration of steroid, we showed rapid & remarkable symptomatic improvement.
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